1. What do we mean by a cardiovascular impairment?
a. We mean
any disorder that affects the proper functioning of the heart or the circulatory system (that is, arteries, veins, capillaries,
and the lymphatic drainage). The disorder can be congenital or acquired.
b. Cardiovascular impairment results from one
or more of four consequences of heart disease:
(i) Chronic heart failure or ventricular dysfunction.
or pain due to myocardial ischemia, with or without necrosis of heart muscle.
(iii) Syncope, or near syncope, due to
inadequate cerebral perfusion from any cardiac cause, such as obstruction of flow or disturbance in rhythm or conduction resulting
in inadequate cardiac output.
(iv) Central cyanosis due to right-to-left shunt, reduced oxygen concentration in the
arterial blood, or pulmonary vascular disease.
c. Disorders of the veins or arteries (for example, obstruction, rupture,
or aneurysm) may cause impairments of the lower extremities (peripheral vascular disease), the central nervous system, the
eyes, the kidneys, and other organs. We will evaluate peripheral vascular disease under 4.11 or 4.12 in part A, and impairments
of another body system(s) under the listings for that body system(s).
2. What do we consider in evaluating cardiovascular
impairments? The listings in this section describe cardiovascular impairments based on symptoms, signs, laboratory findings,
response to a regimen of prescribed treatment, and functional limitations.
3. What do the following terms or phrases
mean in these listings?
a. Medical consultant is an individual defined in §§404.1616(a) and
416.1016(a). This term does not include medical sources who provide consultative examinations for us. We use the abbreviation
“MC” throughout this section to designate a medical consultant.
b. Persistent means that the longitudinal
clinical record shows that, with few exceptions, the required finding(s) has been present, or is expected to be present, for
a continuous period of at least 12 months, such that a pattern of continuing severity is established.
means that the longitudinal clinical record shows that, within a consecutive 12-month period, the finding(s) occurs at least
three times, with intervening periods of improvement of sufficient duration that it is clear that separate events are involved.
Appropriate medically acceptable imaging means that the technique used is the proper one to evaluate and diagnose
the impairment and is commonly recognized as accurate for assessing the cited finding.
e. A consecutive 12-month
period means a period of 12 consecutive months, all or part of which must occur within the period we are considering
in connection with an application or continuing disability review.
f. Currently present means that the finding
is present at the time of adjudication.
g. Uncontrolled means the impairment does not respond adequately to
standard prescribed medical treatment.
B. Documenting Cardiovascular Impairment
1. What basic documentation
do we need? We need sufficiently detailed reports of history, physical examinations, laboratory studies, and any prescribed
treatment and response to allow us to assess the severity and duration of your cardiovascular impairment. A longitudinal clinical
record covering a period of not less than 3 months of observations and treatment is usually necessary, unless we can make
a determination or decision based on the current evidence.
2. Why is a longitudinal clinical record important?
We will usually need a longitudinal clinical record to assess the severity and expected duration of your impairment(s). If
you have a listing-level impairment, you probably will have received medically prescribed treatment. Whenever there is evidence
of such treatment, your longitudinal clinical record should include a description of the ongoing management and evaluation
provided by your treating or other medical source. It should also include your response to this medical management, as well
as information about the nature and severity of
your impairment. The record will provide us with information on your
functional status over an extended period of time and show whether your ability to function is improving, worsening, or unchanging.
What if you have not received ongoing medical treatment?
a. You may not have received ongoing treatment or
have an ongoing relationship with the medical community despite the existence of a severe impairment(s). In this situation,
we will base our evaluation on the current objective medical evidence and the other evidence we have. If you do not receive
treatment, you cannot show an impairment that meets the criteria of these listings. However, we may find you disabled because
you have another impairment(s) that in combination with your cardiovascular impairment medically equals the severity of a
listed impairment or that functionally equals the listings.
b. Unless we can decide your claim favorably on the basis
of the current evidence, a longitudinal record is still important. In rare instances where there is no or insufficient longitudinal
evidence, we may purchase a consultative examination(s) to help us establish the severity and duration of your impairment.
When will we wait before we ask for more evidence?
a. We will wait when we have information showing that your
impairment is not yet stable and the expected change in your impairment might affect our determination or decision. In these
situations, we need to wait to properly evaluate the severity and duration of your impairment during a stable period. Examples
of when we might wait are:
(i) If you have had a recent acute event; for example, acute rheumatic fever.
If you have recently had a corrective cardiac procedure; for example, open-heart surgery.
(iii) If you have started
new drug therapy and your response to this treatment has not yet been established; for example, beta-blocker therapy for dilated
b. In these situations, we will obtain more evidence 3 months following the event before
we evaluate your impairment. However, we will not wait if we have enough information to make a determination or decision based
on all of the relevant evidence in your case.
5. Will we purchase any studies? In appropriate situations, we
will purchase studies necessary to substantiate the diagnosis or to document the severity of your impairment, generally after
we have evaluated the medical and other evidence we already have. We will not purchase studies involving exercise testing
if there is significant risk involved or if there is another medical reason not to perform the test. We will follow sections
4.00C6, 4.00C7, 4.00C8, and 104.00B7 when we decide whether to purchase exercise testing. We will make a reasonable effort
to obtain any additional studies from a qualified medical source in an office or center experienced in pediatric cardiac assessment.
6. What studies will we not purchase? We will not purchase any studies involving cardiac
catheterization, such as coronary angiography, arteriograms, or electrophysiological studies. However, if the results of catheterization
are part of the existing evidence we have, we will consider them together with the other relevant evidence. See 4.00C15a in
7. Will we use exercise tolerance tests (ETTs) for evaluating children with cardiovascular impairment?
ETTs, though increasingly used, are still less frequently indicated in children than in adults, and can rarely be performed
successfully by children under 6 years of age. An ETT may be of value in the assessment of some arrhythmias, in the assessment
of the severity of chronic heart failure, and in the assessment of recovery of function following cardiac surgery or other
b. We will purchase an ETT in a childhood claim only if we cannot make a determination or decision based
on the evidence we have and an MC, preferably one with experience in the care of children with cardiovascular impairments,
has determined that an ETT is needed to evaluate your impairment. We will not purchase an ETT if you are less than 6 years
of age. If we do purchase an ETT for a child age 12 or younger, it must be performed by a qualified medical source in a specialty
center for pediatric cardiology or other facility qualified to perform exercise tests of children.
c. For full details
on ETT requirements and usage, see 4.00C in part A.
C. Evaluating Chronic Heart Failure
1. What is chronic
heart failure (CHF)?
a. CHF is the inability of the heart to pump enough oxygenated blood to body tissues.
This syndrome is characterized by symptoms and signs of pulmonary or systemic congestion (fluid retention) or limited cardiac
output. Certain laboratory findings of cardiac functional and structural abnormality support the diagnosis of CHF.
CHF is considered in these listings as a single category whether due to atherosclerosis (narrowing of the arteries), cardiomyopathy,
hypertension, or rheumatic, congenital, or other heart disease. However, if the CHF is the result of primary pulmonary hypertension
secondary to disease of the lung (cor pulmonale), we will evaluate your impairment using 3.09 in the respiratory system listings
in part A.
2. What evidence of CHF do we need?
a. Cardiomegaly or ventricular dysfunction must be present
and demonstrated by appropriate medically acceptable imaging, such as chest x-ray, echocardiography (M-Mode, 2-dimensional,
and Doppler), radionuclide studies, or cardiac catheterization.
(i) Cardiomegaly is present when:
Left ventricular diastolic dimension or systolic dimension is greater than 2 standard deviations above the mean for the child's
body surface area;
(B) Left ventricular mass is greater than 2 standard deviations above the mean for the
child's body surface area; or
(C) Chest x-ray (6 foot PA film) is indicative of cardiomegaly if the cardiothoracic
ratio is over 60 percent at 1 year of age or less, or 55 percent or greater at more than 1 year of age.
dysfunction is present when indices of left ventricular function, such as fractional shortening or ejection fraction (the
percentage of the blood in the ventricle actually pumped out with each contraction), are greater than 2 standard deviations
below the mean for the child's age. (Fractional shortening, also called shortening fraction, reflects the left ventricular
systolic function in the absence of segmental wall motion abnormalities and has a linear correlation with ejection fraction.
In children, fractional shortening is more commonly used than ejection fraction.)
(iii) However, these measurements
alone do not reflect your functional capacity, which we evaluate by considering all of the relevant evidence.
findings on appropriate medically acceptable imaging may include increased pulmonary vascular markings, pleural effusion,
and pulmonary edema. These findings need not be present on each report, since CHF may be controlled by prescribed treatment.
To establish that you have chronic heart failure, your medical history and physical examination should describe characteristic
symptoms and signs of pulmonary or systemic congestion or of limited cardiac output associated with the abnormal findings
on appropriate medically acceptable imaging. When an acute episode of heart failure is triggered by a remediable factor, such
as an arrhythmia, dietary sodium overload, or high altitude, cardiac function may be restored and a chronic impairment may
not be present.
(i) Symptoms of congestion or of limited cardiac output include easy fatigue, weakness, shortness of
breath (dyspnea), cough, or chest discomfort at rest or with activity. Children with CHF may also experience shortness of
breath on lying flat (orthopnea) or episodes of shortness of breath that wake them from sleep (paroxysmal nocturnal dyspnea).
They may also experience cardiac arrhythmias resulting in palpitations, lightheadedness, or fainting. Fatigue or exercise
intolerance in an infant may be manifested by prolonged feeding time, often associated with excessive respiratory effort and
(ii) During infancy, other manifestations of chronic heart failure may include failure to gain weight or involuntary
loss of weight and repeated lower respiratory tract infections.
(iii) Signs of congestion may include hepatomegaly,
ascites, increased jugular venous distention or pressure, rales, peripheral edema, rapid shallow breathing (tachypnea), or
rapid weight gain. However, these signs need not be found on all examinations because fluid retention may be controlled by
D. Evaluating Congenital Heart Disease
1. What is congenital heart disease? Congenital
heart disease is any abnormality of the heart or the major blood vessels that is present at birth. Examples include:
Abnormalities of cardiac septation , including ventricular septal defect or atrioventricular canal;
resulting in cyanotic heart disease , including tetralogy of Fallot or transposition of the great arteries;
Valvular defects or obstructions to ventricular outflow, including pulmonary or aortic stenosis or coarctation of
the aorta; and
d. Major abnormalities of ventricular development , including hypoplastic left heart syndrome
or pulmonary tricuspid atresia with hypoplastic right ventricle.
2. How will we evaluate symptomatic congenital
a. Because of improved treatment methods, more children with congenital heart disease are living
longer. Although some types of congenital heart disease may be corrected by surgery, many children with treated congenital
heart disease continue to have problems throughout their lives (symptomatic congenital heart disease). If you have congenital
heart disease that results in chronic heart failure with evidence of ventricular dysfunction or in recurrent arrhythmias,
we will evaluate your impairment under 104.02 or 104.05. Otherwise, we will evaluate your impairment under 104.06.
For 104.06A2, we will accept pulse oximetry measurements instead of arterial O 2, but the arterial O 2 values are preferred,
c. For 104.06D, examples of impairments that in most instances will require life-saving surgery or a combination
of surgery and other major interventional procedures (for example, multiple “balloon” catheter procedures) before
age 1 include, but are not limited to, the following:
(i) Hypoplastic left heart syndrome,
(ii) Critical aortic
stenosis with neonatal heart failure,
(iii) Critical coarctation of the aorta, with or without associated anomalies,
Complete atrioventricular canal defects,
(v) Transposition of the great arteries,
(vi) Tetralogy of Fallot,
Pulmonary atresia with intact ventricular septum,
(viii) Single ventricle,
(ix) Tricuspid atresia, and
Multiple ventricular septal defects.
E. Evaluating Arrhythmias
1. What is an arrhythmia? An arrhythmia
is a change in the regular beat of the heart. Your heart may seem to skip a beat or beat irregularly, very quickly (tachycardia),
or very slowly (bradycardia).
2. What are the different types of arrhythmias?
a. There are many types
of arrhythmias. Arrhythmias are identified by where they occur in the heart (atria or ventricles) and by what happens to the
heart's rhythm when they occur.
b. Arrhythmias arising in the cardiac atria (upper chambers of the heart) are called
atrial or supraventricular arrhythmias. Ventricular arrhythmias begin in the ventricles (lower chambers). In general, ventricular
arrhythmias caused by heart disease are the most serious.
3. How do we evaluate arrhythmias using 104.05?
We will use 104.05 when you have arrhythmias that are not fully controlled by medication, an implanted pacemaker, or an implanted
cardiac defibrillator and you have uncontrolled recurrent episodes of syncope or near syncope. If your arrhythmias are controlled,
we will evaluate your underlying heart disease using the appropriate listing. For other considerations when we evaluate arrhythmias
in the presence of an implanted cardiac defibrillator, see 104.00E4.
b. We consider near syncope to be a period
of altered consciousness, since syncope is a loss of consciousness or a faint. It is not merely a feeling of light-headedness,
momentary weakness, or dizziness.
c. For purposes of 104.05, there must be a documented association between the syncope
or near syncope and the recurrent arrhythmia. The recurrent arrhythmia, not some other cardiac or non-cardiac disorder, must
be established as the cause of the associated symptom. This documentation of the association between the symptoms and the
arrhythmia may come from the usual diagnostic methods, including Holter monitoring (also called ambulatory electrocardiography)
and tilt-table testing with a concurrent ECG. Although an arrhythmia may be a coincidental finding on an ETT, we will not
purchase an ETT to document the presence of a cardiac arrhythmia.
4. What will we consider when you have an implanted
cardiac defibrillator and you do not have arrhythmias that meet the requirements of 104.05?
a. Implanted cardiac
defibrillators are used to prevent sudden cardiac death in children who have had, or are at high risk for, cardiac arrest
from life-threatening ventricular arrhythmias. The largest group of children at risk for sudden cardiac death consists of
children with cardiomyopathy (ischemic or non-ischemic) and reduced ventricular function. However, life-threatening ventricular
arrhythmias can also occur in children with little or no ventricular dysfunction. The shock from the implanted cardiac defibrillator
is a unique form of treatment; it rescues a child from what may have been cardiac arrest. However, as a consequence of the
shock(s), children may experience psychological distress, which we may evaluate under the mental disorders listings in 112.00ff.
Most implantable cardiac defibrillators have rhythm-correcting and pacemaker capabilities. In some children, these functions
may result in the termination of ventricular arrhythmias without an otherwise painful shock. (The shock is like being kicked
in the chest.) Implanted cardiac defibrillators may deliver inappropriate shocks, often repeatedly, in response to benign
arrhythmias or electrical malfunction. Also, exposure to strong electrical or magnetic fields, such as from MRI (magnetic
resonance imaging), can trigger or reprogram an implanted cardiac defibrillator, resulting in inappropriate shocks. We must
consider the frequency of, and the reason(s) for, the shocks when evaluating the severity and duration of your impairment.
In general, the exercise limitations imposed on children with an implanted cardiac defibrillator are those dictated by the
underlying heart impairment. However, the exercise limitations may be greater when the implanted cardiac defibrillator delivers
an inappropriate shock in response to the increase in heart rate with exercise, or when there is exercise-induced ventricular
F. Evaluating other cardiovascular impairments
1. What is ischemic heart disease (IHD) and how
will we evaluate it in children? IHD results when one or more of your coronary arteries is narrowed or obstructed or,
in rare situations, constricted due to vasospasm, interfering with the normal flow of blood to your heart muscle (ischemia).
The obstruction may be the result of an embolus, a thrombus, or plaque. When heart muscle tissue dies as a result of the reduced
blood supply, it is called a myocardial infarction (heart attack). Ischemia is rare in children, but when it occurs, its effects
on children are the same as on adults. If you have IHD, we will evaluate it under 4.00E and 4.04 in part A.
will we evaluate hypertension? Because hypertension (high blood pressure) generally causes disability through
its effects on other body systems, we will evaluate it by reference to the specific body system(s) affected (heart, brain,
kidneys, or eyes) when we consider its effects under the listings. We will also consider any limitations imposed by your hypertension
when we consider whether you have an impairment that functionally equals the listings.
3. What is cardiomyopathy
and how will we evaluate it? Cardiomyopathy is a disease of the heart muscle. The heart loses its ability to pump blood
(heart failure), and in some instances, heart rhythm is disturbed, leading to irregular heartbeats (arrhythmias). Usually,
the exact cause of the muscle damage is never found (idiopathic cardiomyopathy). There are various types of cardiomyopathy,
which fall into two major categories: Ischemic and nonischemic cardiomyopathy. Ischemic cardiomyopathy typically
refers to heart muscle damage that results from coronary artery disease, including heart attacks. Nonischemic cardiomyopathy
includes several types: Dilated, hypertrophic, and restrictive. We will evaluate cardiomyopathy under 4.04 in part A, 104.02,
104.05, or 111.06, depending on its effects on you.
4. How will we evaluate valvular heart disease? We will
evaluate valvular heart disease under the listing appropriate for its effect on you. Thus, we may use 4.04 in part A, 104.02,
104.05, 104.06, or an appropriate neurological listing in 111.00ff.
5. What do we consider when we evaluate heart
a. After your heart transplant, we will consider you disabled for 1 year following the surgery
because there is a greater likelihood of rejection of the organ and infection during the first year.
b. However, heart
transplant patients generally meet our definition of disability before they undergo transplantation. We will determine the
onset of your disability based on the facts in your case.
c. We will not assume that you became disabled when your name
was placed on a transplant waiting list. This is because you may be placed on a waiting list soon after diagnosis of the cardiac
disorder that may eventually require a transplant. Physicians recognize that candidates for transplantation often have to
wait months or even years before a suitable donor heart is found, so they place their patients on the list as soon as permitted.
When we do a continuing disability review to determine whether you are still disabled, we will evaluate your residual impairment(s),
as shown by symptoms, signs, and laboratory findings, including any side effects of medication. We will consider any remaining
symptoms, signs, and laboratory findings indicative of cardiac dysfunction in deciding whether medical improvement (as defined
in §416.994a) has occurred.
6. How will we evaluate chronic rheumatic fever or rheumatic heart disease?
The diagnosis should be made in accordance with the current revised Jones criteria for guidance in the diagnosis of rheumatic
fever. We will evaluate persistence of rheumatic fever activity under 104.13. If you have evidence of chronic heart failure
or recurrent arrhythmias associated with rheumatic heart disease, we will use 104.02 or 104.05.
7. What is hyperlipidemia
and how will we evaluate it? Hyperlipidemia is the general term for an elevation of any or all of the lipids (fats or
cholesterol) in the blood; for example, hypertriglyceridemia, hypercholesterolemia, and hyperlipoproteinemia. These disorders
of lipoprotein metabolism and transport can cause defects throughout the body. The effects most likely to interfere with function
are those produced by atherosclerosis (narrowing of the arteries) and coronary artery disease. We will evaluate your lipoprotein
disorder by considering its effects on you.
8. How will we evaluate Kawasaki disease? We will evaluate Kawasaki
disease under the listing appropriate to its effects on you, which may include major coronary artery aneurysm or heart failure.
A major coronary artery aneurysm may cause ischemia or arrhythmia, which we will evaluate under 4.04 in part A or 104.05.
We will evaluate chronic heart failure under 104.02.
9. What is lymphedema and how will we evaluate it?
Lymphedema is edema of the extremities due to a disorder of the lymphatic circulation; at its worst, it is called
elephantiasis. Primary lymphedema is caused by abnormal development of lymph vessels and may be present at birth (congenital
lymphedema), but more often develops during the teens (lymphedema praecox). Secondary lymphedema is due to obstruction or
destruction of normal lymphatic channels due to tumor, surgery, repeated infections, or parasitic infection such as filariasis.
Lymphedema most commonly affects one extremity.
b. Lymphedema does not meet the requirements of 4.11 in part A, although
it may medically equal the severity of that listing. We will evaluate lymphedema by considering whether the underlying cause
meets or medically equals any listing or whether the lymphedema medically equals a cardiovascular listing, such as 4.11, or
a musculoskeletal listing, such as 101.02A or 101.03. If no listing is met or medically equaled, we will evaluate any functional
limitations imposed by your lymphedema when we consider whether you have an impairment that functionally equals the listings.
What is Marfan syndrome and how will we evaluate it?
a. Marfan syndrome is a genetic connective tissue disorder
that affects multiple body systems, including the skeleton, eyes, heart, blood vessels, nervous system, skin, and lungs. There
is no specific laboratory test to diagnose Marfan syndrome. The diagnosis is generally made by medical history, including
family history, physical examination, including an evaluation of the ratio of arm/leg size to trunk size, a slit lamp eye
examination, and a heart test(s), such as an echocardiogram. In some cases, a genetic analysis may be useful, but such analyses
may not provide any additional helpful information.
b. The effects of Marfan syndrome can range from mild to severe.
In most cases, the disorder progresses as you age. Most individuals with Marfan syndrome have abnormalities associated with
the heart and blood vessels. Your heart’s mitral valve may leak, causing a heart murmur. Small leaks may not cause symptoms,
but larger ones may cause shortness of breath, fatigue, and palpitations. Another effect is that the wall of the aorta may
be weakened and stretch (aortic dilation). This aortic dilation may tear, dissect, or rupture, causing serious heart problems
or sometimes sudden death. We will evaluate the manifestations of your Marfan syndrome under the appropriate body system criteria,
such as 4.10 in part A, or if necessary consider the functional limitations imposed by your impairment.
G. Other Evaluation
1. What effect does obesity have on the cardiovascular system and how will we evaluate it? Obesity is
a medically determinable impairment that is often associated with disorders of the cardiovascular system. Disturbance of this
system can be a major cause of disability in children with obesity. Obesity may affect the cardiovascular system because of
the increased workload the additional body mass places on the heart. Obesity may make it harder for the chest and lungs to
expand. This can mean that the respiratory system must work harder to provide needed oxygen. This in turn would make the heart
work harder to pump blood to carry oxygen to the body. Because the body would be working harder at rest, its ability to perform
additional work would be less than would otherwise be expected. Thus, the combined effects of obesity with cardiovascular
impairments can be greater than the effects of each of the impairments considered separately. We must consider any additional
and cumulative effects of obesity when we determine whether you have a severe cardiovascular impairment or a listing-level
cardiovascular impairment (or a combination of impairments that medically equals a listing), and when we determine whether
your impairment(s) functionally equals the listings.
2. How do we relate treatment to functional status? In
general, conclusions about the severity of a cardiovascular impairment cannot be made on the basis of type of treatment rendered
or anticipated. The amount of function restored and the time required for improvement after treatment (medical, surgical,
or a prescribed program of progressive physical activity) vary with the nature and extent of the disorder, the type of treatment,
and other factors. Depending upon the timing of this treatment in relation to the alleged onset date of disability, we may
need to defer evaluation of the impairment for a period of up to 3 months from the date treatment began to permit consideration
of treatment effects, unless we can make a determination or decision using the evidence we have. See 104.00B4.
do we evaluate impairments that do not meet one of the cardiovascular listings?
a. These listings are only examples
of common cardiovascular disorders that we consider severe enough to result in marked and severe functional limitations. If
your severe impairment(s) does not meet the criteria of any of these listings, we must also consider whether you have an impairment(s)
that satisfies the criteria of a listing in another body system.
b. If you have a severe medically determinable impairment(s)
that does not meet a listing, we will determine whether your impairment(s) medically equals a listing. (See §416.926.)
If you have a severe impairment(s) that does not meet or medically equal the criteria of a listing, we will consider whether
it functionally equals the listings. (See §416.926a.) When we decide whether you continue to be disabled, we use the
rules in §416.994a.
104.01 Category of Impairments, Cardiovascular System
104.02 Chronic heart failure. while on a regimen of prescribed treatment with symptoms and signs
described in 104.00C2 and with one of the following:
A. Persistent tachycardia at rest (see Table I);
Persistent tachypnea at rest (see Table II) or markedly decreased exercise tolerance (see 104.00C2b);
1. An involuntary weight loss or failure to gain weight at an appropriate rate for age, resulting
in a fall of 15 percentiles from an established growth curve (on current NCHS/CDC growth chart) which is currently present
(see 104.00A3f) and has persisted for 2 months or longer; or
2. An involuntary weight loss or failure to gain weight
at an appropriate rate for age, resulting in a fall to below the third percentile from an established growth curve (on current
NCHS/CDC growth chart) which is currently present (see 104.00A3f) and has persisted for 2 months or longer.
Table I - Tachycardia at rest
Apical Heart Rate (Beats Per Minute)
. . . . 150
1 through 3 years
. . . . 130
4 through 9 years
. . . 120
10 through 15 years
. . . . 110
Over 15 years
. . . . 100
Table II - Tachypnea at rest
Respiratory Rate Over (Per Minute)
Under 1 year
. . . . 40
1 through 5 years
. . . . . 35
6 through 9 years
. . . . . 30
Over 9 years
. . . . . 25
104.05 Recurrent arrhythmias, not related to reversible causes such as electrolyte abnormalities
or digitalis glycoside or antiarrhythmic drug toxicity, resulting in uncontrolled (see 104.00A3g), recurrent (see 104.00A3c)
episodes of cardiac syncope or near syncope (see 104.00E3b), despite prescribed treatment (see 104.00B3 if there is no prescribed
treatment), and documented by resting or ambulatory (Holter) electrocardiography, or by other appropriate medically acceptable
testing, coincident with the occurrence of syncope or near syncope (see 104.00E3c).
104.06 Congenital heart disease documented by appropriate medically acceptable imaging (see 104.00A3d) or
cardiac catheterization, with one of the following:
A. Cyanotic heart disease, with persistent, chronic hypoxemia as
1. Hematocrit of 55 percent or greater on two evaluations 3 months or more apart within a consecutive
12-month period (see 104.00A3e); or
2. Arterial O 2 saturation of less than 90 percent in room air, or resting arterial
PO 2 of 60 Torr or less; or
3. Hypercyanotic spells, syncope, characteristic squatting, or other incapacitating symptoms
directly related to documented cyanotic heart disease; or
4. Exercise intolerance with increased hypoxemia on exertion.
Secondary pulmonary vascular obstructive disease with pulmonary arterial systolic pressure elevated to at least 70 percent
of the systemic arterial systolic pressure.
C. Symptomatic acyanotic heart disease, with ventricular dysfunction
interfering very seriously with the ability to independently initiate, sustain, or c omplete activities.
infants under 12 months of age at the time of filing, with life-threatening congenital heart impairment that will require
or already has required surgical treatment in the first year of life, and the impairment is expected to be disabling (because
of residual impairment following surgery, or the recovery time required, or both) until the attainment of at least 1 year
of age, consider the infant to be under disability until the attainment of at least age 1; thereafter, evaluate impairment
severity with reference to the appropriate listing.
104.09 Heart transplant. Consider under a disability for 1 year following surgery; thereafter,
evaluate residual impairment under the appropriate listing.
104.13 Rheumatic heart disease, with persistence of rheumatic fever activity manifested by significant murmurs(s),
cardiac enlargement or ventricular dysfunction (see 104.00C2a), and other associated abnormal laboratory findings; for example,
an elevated sedimentation rate or ECG findings, for 6 months or more in a consecutive 12-month period (see 104.00A3e). Consider
under a disability for 18 months from the established onset of impairment, then evaluate any residual impairment(s).